Wunderlich's syndrome, or spontaneous non-traumatic retroperitoneal hemorrhage, can be a life-threatening event.
Renal angiomyolipoma is a rare benign tumor that can occur sporadically, or in association with tuberous sclerosis. A
case of spontaneous retroperitoneal hemorrhage in a patient with tuberous sclerosis and renal angiomyolipoma is
presented. Tuberous sclerosis complex is a rare symptom complex and may have varied presentations.We present a
case of hypovolemic shock due to spontaneous rupture of large angiomyolipoma in a 24-year-old male patient with
tuberous sclerosis complex (TSC).The hemodynamic instability of our patient leads to an urgent surgery and right
nephrectomy was done for the angiomyolipomas. Spontaneous hemorrhage in renal angiomyolipoma in a case of
tuberous sclerosis and management are discussed.
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