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Background:Presence of teeth in a neonate is a rare occurrence due to the disturbance in the biological chronology of teeth. Although uncommon, these teeth if present are found to have several clinical implications.Aims:This study aimed to describe the clinical characteristics and the treatment outcome of natal and neonatal teeth from a hospital setting.Materials and Methods:This retrospective study was carried out by reviewing the hospital records of babies with natal or neonatal teeth in a tertiary hospital in Tamil Nadu between January 1, 2012, and December 31, 2014. Babies with complete clinical data along with their follow-up records were selected and results were analyzed.Results:Complete clinical data of 33 babies with a total of 52 teeth were included, of which 28 teeth were natal and 24 teeth were neonatal. All the teeth were located in the mandibular primary incisor region and majority were in pairs. A positive family history was present in eight cases. Extractions were carried out only in cases where the teeth were found to be extremely loose or interfering with feeding. The only local complication noted in this study was Riga–Fede disease.Conclusions:The findings of this study suggest that natal and neonatal teeth may have a possible hereditary basis. All the teeth were noted to be prematurely erupted primary teeth rather than supernumerary teeth. Both dentists and pediatricians need to be aware of the clinical implications of these teeth and that they should be retained unless they are symptomatic.

This study demonstrates a high prevalence of untimely primary teeth extractions in young children and dental caries continues to be the leading cause. It clearly reflects on the lack of infant oral health care, the inadequacy of awareness and underutilization of oral health services among children in India.

Hajdu-Cheney Syndrome is a rare genetic disorder characterised by progressive focal bone destruction. It is known to be an autosomal dominant disorder but there have been reports of sporadic cases as well. Although the disease manifestation is found to begin from birth, it is most often not diagnosed until adolescence or adulthood. It could be due to the rarity of the condition and the variation of the disease manifestation at different age groups. We report a case of Hajdu-Cheney Syndrome in a 26-year-old male who presented with severe periodontitis and premature loss of teeth. The other characteristic features included craniofacial dysmorphism, abnormalities of the digits and dental anomalies. Patients with craniofacial dysmorphism along with dental abnormalities should be thoroughly examined for any underlying systemic disorder. A team of specialists may be able to diagnose this condition before the disease is advanced.

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