Hadjdu-Cheney syndrome is a rare type of syndrome characterized by acro-osteolysis, dolichocephaly with multiple Wormian bones, absence of frontal sinuses and joint laxity. A case of this syndrome is presented. A histological study of the osteolytic lesion revealed destruction characterized by microfractures with a poor reparative process. It is postulated that an abnormality of osteoblast or osteoid function is the pathogenesis of this syndrome.
There have been several reports of osteomalacia or CASE REPORTS late rickets associated with a tumour of bone or soft tissue, the removal ofwhich resulted in either cure ofthe Case 1-A Japanese worker aged eighteen was admitted to ourTokyo University Branch Hospital in December 1974 with osteomalacia or improvement in its clinical course. In a five-year history of difficulty in walking and a swelling over the dorsal aspect of the right hand. He had first noticed the swelling at the age of thirteen and at the same time began to feel weakness and instability of the knees when he took outdoor exercise. Over the next year the weakness progressed to such a degree that he was unable to run or to rise from the
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