the pathological area (epiphyseal, metaphyseal, diaphyseal) of the bone. Disorders are named as spondyloepiphyseal dysplasia (SED) when the pathology is in the vertebral epiphysis [1]. SED is defined as 3 clinic groups: 1-SED congenita 2-SED tarda 3-SED tarda with progressive arthropathy (SEDT-PA) [2]. The skeletal dysplasias are genetically heteroge neous and SEDT usually inherited as X-linked recessive. It is characterized by short trunk and extremities, deformity of the vertebraes, platyspondyly, kyphoscoliosis, coxa vara, genu valgum-varum, abnormal shape and structure of the epiphyses of hand bones. Boys are affected more often [1-3]. Although the one set of SEDT-PA is 3 and 6 years of age, they are diagnosed at an older age. Because of joint involvement SEDT-PA may be confused with juvenile idiopathic arthritis and SEDT-PA also called progressive pseudo rheumatoidarthropathy of childhood [4][5][6].
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