Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive disorder. The oral manifestations of the syndrome include rapidly progressive periodontal disease resulting in premature exfoliation of primary and permanent dentitions. Patients are often edentulous at an early age and require prosthodontic treatment. This report is the oral rehabilitation of an edentulous 21-year-old woman with PLS. Treatment included maxillary and mandibular fixed prostheses supported by osseointegrated dental implants. At the 4-year follow-up, the patient presented significant improvements in oral function and psychosocial activities and no prosthetic complications.
This clinical report describes a noninvasive approach for the treatment of a patient diagnosed with amelogenesis imperfecta (AI) and severe anterior open bite. The patient's functional and esthetic expectations were successfully met with a transitional overlay removable partial denture.Amelogenesis imperfecta (AI) is an inherited disease that disturbs the formation of enamel.1,2 There are three types of AI: hypoplasia, hypocalcification, and hypomaturation.
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