Dorsal pancreatic agenesis is an extremely rare developmental anomaly of gastrointestinal system. It is mostly an incidental finding and detected in adulthood. Pancreatic anomaly associated with renal positional defect is very rare association. We have reported a case of complete dorsal pancreas agenesis associated with crossed renal ectopia in a 30year-old gentleman who was investigated for gastric malignancy. Contrast enhanced computed tomography (CECT) abdomen is an important imaging to see the anomalous pancreas, abnormal renal position and evaluation of gastric malignancy for its further management. Upper abdominal magnetic resonance imaging (MRI) and magnetic resonance cholangiopancreatography (MRCP) is a non-invasive imaging to see the pancreatic duct.
ARTICLE INFO ABSTRACTVon Hippel Lindau disease (VHL) is a rare, autosomal dominant inherited multisystem disorder which can be diagnosed by clinical, radiologic and genetic findings (Katabathina et al, 2014). We reported the spectrum of CT and MR imaging findings of sporadic VHL and familial VHL in three patients. Recurrent headache, ataxia and abdominal pain are most common symptoms. Multiple cerebellar hemangioblastomas are present in all the patients. Pancreatic serous cystadenoma, renal cysts and spinal syrinx formation was demonstrated in 33year old sporadic VHL patient.
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