A survey of 56 patients aged ≤ 16 years, admitted (1954–1979) for cerebral arteriovenous malformations, is presented. The clinical manifestation was mostly related to hemorrhage, less frequently to epilepsy or to a cerebral ‘steal’ syndrome. The most frequent site was the parietal lobe, with supply from the middle cerebral artery. Deep malformations were not uncommon and most lesions were of medium or large size. 38 patients were operated upon, and 18 were given treatment other than surgical (including radiotherapy). 23 malformations were completely excised, in 4 patients only a partial excision could be carried out, and in 10 patients surgery consisted of occlusion (clipping or coagulation) of feeding vessels. In 1 patient, surgery had to be limited to removal of an intracerebral hematoma. The immediate and long-term results of treatment are much better in the surgical than in the nonsurgical group.

✓ A case of multiple neurinomas, firmly embedded within the nervous substance of the spinal cord and presumably extending over the entire length of its surface, is reported. The complete lack of relationship of the multiple lesions with the spinal roots and the absence of signs of neurofibromatosis are the most salient features of this uncommon case. In a discussion on the origin of the condition, it is concluded that this case might be an example of neurocristopathy.