The cataract is one of leading causes of low vision and blindness in the world. It is well known that a significant decreasing of vision or its total loss result in deterioration of quality of life, including total or partial loss of working capacity. On the basis of official statistics data, a study was carried out шт the course of which costs of inputs to cataract treatment and dependence of disability on quality of visual functions were established.
The review presents the pathogenetic, diagnostic, therapeutic and rehabilitation aspects of computerized visual syndrome (CVS). The importance of an integrated approach to the implementation of treatment and rehabilitation measures is emphasized. The promising directions of scientific and practical activity on the
problem of treating patients with GLC symptoms from the standpoint of modern requirements for medical rehabilitation have been determined.
В статье предлагаются доработанные рекомендации по организации действий органов государственной власти и органов местного самоуправления при ликвидации чрезвы-чайных ситуаций. Они разработаны с учетом требований федеральных законов, поста-новлений Правительства Российской Федерации, нормативных правовых актов Мини-стерства Российской Федерации по делам гражданской обороны, чрезвычайным ситуа-циям и ликвидации последствий стихийных бедствий (МЧС России) и других феде-ральных органов исполнительной власти. Предназначены для оказания практической помощи территориальным органам МЧС России, федеральным органам исполнитель-ной власти, органам исполнительной власти субъектов Российской Федерации, органам местного самоуправления и организациям в решении вопросов организации первооче-редного жизнеобеспечения населения в чрезвычайных ситуациях и работы пунктов временного размещения пострадавшего населения.Ключевые слова: координационные органы ликвидации ЧС; мониторинг социаль-ных проблем ОПБ населения РФ, критическая ситуация, качественный уровень госу-дарственного пожарного надзора, структуризация проблем, мероприятий жизнеобес-печения DOI: 10.17212/2307-6879-2017-2-113-119 Статья получена 26 апреля 2017 г.
The atypical hemolytic uremic syndrome (aHUS) is an ultra-rare disease with a genetically determined dysregulation of the alternative complement pathway, which leads to the development of thrombotic microangiopathy. The application of the targeted therapy in Russia has changed the natural course of the disease since 2012: from death of a patient to achieving a long-term remission of the aHUS. The authors report the clinical case of the aHUS associated with a heterozygous mutation in CFH gene c.2850G>T (p.Gln950His) in a 2 years and 2 months old pediatric patient. The difficulty in diagnosing of the aHUS was the lack of specific laboratory criteria confirming the diagnosis as well as the presence of a diarrheal prodrome at the onset. The diagnosis has been made on the basis of the development of microangiopathic hemolytic anemia, thrombocytopenia, acute kidney injury and the exclusion of other forms of thrombotic microangiopathy. The treatment of the patient in accordance with the clinical guidelines for the management of patients with this nosology proved to be effective and led to a stable remission of the aHUS, which also confirmed the correctness of the diagnosis. The described clinical case observation is of interest to pediatrician physicians and nephrologists. The important factors in the management of such patients are the timely diagnosis of the aHUS along with the initiation of complement-inhibiting Eculizumab therapy.
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