No abstract

Nephrotic syndrome is mostly idiopathic but secondary causes are also not uncommon. In our case we had a steroid resistance case so on renal biopsy we found that it due to amyloidosis which was also attributed to systemic JIA. It showed response to biological agents.

8p deletion is a multisystem congenital disorder manifesting since early infancy with global developmental delay and other organ involvement. In our case the presentation was at 6 months with back deformity and developmental delay, dysmorphism and on further evaluation we found various structural anomalies. It needs a regular follow for early pick up of the associated comorbidities.