Background
Double Chambered Left Ventricle is a very rare congenital cardiac condition with limited cases reported in literature, etiology of which is obscure and presentation can be varied.
Aim of the study
To share our experience of two diverse cases of Double Chambered Left Ventricle at our institute.
Results
Two diverse cases of Double Chambered Left Ventricle were appropriately diagnosed and successfully managed. One of which one was congenital and the other was acquired
Methods
Both the patients had an uneventful peri‐operative period.
Conclusions
Double Chambered Left Ventricle is a condition which remains an enigma. Diagnosis requires a high degree of radiological suspicion for prompt diagnosis and good surgical outcomes.
Herein, we present a case of Berry syndrome with successful surgical repair in an infant. A definitive diagnosis was established with appropriate investigative modalities, and a single-stage repair was performed with good results.
Background
Persistent left superior vena cava is a well-recognized thoracic venous abnormality, most of which do not present with any symptoms. Its opening into the left atrium is uncommonly encountered and, if present, is noted to be associated with various other complex intracardiac malformations, which further complicates its management. Herein, we highlight a case of an adult with persistent left superior vena cava with a spectrum of other cardiac anomalies rarely encountered with it, which was effectively managed by tailored surgical intervention.
Case presentation
A 26-year-old female on meticulous evaluation was found to have left isomerism with an interrupted inferior vena cava and hemiazygos continuing as a persistent left superior vena cava. It was also associated with common atrium, partial atrioventricular canal defect, and complete heart block. This complex array of anomalies was managed surgically. Common atrium was closed with atrial neo-septation using autologous pericardial patch tailored in a way, such that the persistent left superior vena cava drained into right atrium with left atrial appendage being on right side of neo-septum. Cleft in the left atrioventricular valve was also repaired. Despite preoperative complete heart block, the patient had an uneventful postoperative recovery and was in atrial fibrillation with controlled ventricular rate, thus precluding the need for permanent pacemaker implantation.
Conclusions
A rare spectrum of adult congenital cyanotic heart disease was successfully managed with thorough preoperative evaluation and judicious intraoperative management. Surgical management should be tailored based on specific anatomy for reduction of morbidity and optimum results.
Background: We report a series of 7 patients of right pulmonary artery to left atrium fistula operated in our institute between 1998 and 2019.
Aim of the Study:To present a comprehensive management of right pulmonary artery to left atrium fistula in an organised manner with excellent results, even in adult population.Methods: Seven consecutive patients of RPA to LA fistula were investigated with appropriate diagnostic modalities and underwent successful surgical correction.Results: Post procedure the oxygen saturation improved to >95% in all the patients. There were no early or late post-operative deaths. All patients underwent TTE at every follow up.Conclusion: Appropriate use of imaging techniques helps in exact diagnosis with anatomical delineation which decides the further line of management in relieving the symptoms and prevention of complications of the fistula.
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.