Angiomyolipoma (AML) is a tumor that is composed of blood vessels, adipose tissue and smooth muscle. Mostly it occurs in kidney and also to those 80% of patients associate with tubular sclerosis. AML which is developed in the nasal cavity shows varies characteristics than when it happens in kidney or liver. It does not carry nodular sclerosis and its size is smaller than the one which is developed in kidney or liver, mostly less than 4 cm. There is no epithelioid smooth muscle cell and HMB-45 stain is completely negative. In the nasal cavity, angiomyolipoma has been rarely reported in the literature. We present a case of angiomyolipoma in the nasal cavity.
Background: Creutzfeldt-Jakob disease (CJD) is the prototype of a family of rare and fatal human degenerative conditions characterized by rapidly progressive dementia, myoclonus and akinetic mutism. Methods: A 70-year-old man with a long history of alcoholism was admitted to the hospital due to acute onset confusion, delirium, bilateral lateral gaze palsy, and gait disturbance. He was administered intravenously with thiamine for 10 days under suspicion of Wernicke encephalopathy, but there was no improvement of clinical symptoms. On the 11th day after admission, the patient presented with myoclonus, apathy and akinetic mutism. His cerebrospinal fluid was positive for 14-3-3 protein. The patient was finally diagnosed as probable Creutzfeldt-Jakob disease.
Conclusion:We reported a case of Creutzfeldt-Jakob disease mimicking Wernicke encephalopathy.
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