In this case study, a 33-year-old male presented initially to our clinic in 1989 with a soft tissue mass on his left posterior chest wall that had previously been debulked 3 times beginning in 1973. Pathology from these previous excisions confirmed a spindle cell hemangioendothelioma. Following the previous excisions, the mass recurred and slowly increased in size but did not cause any serious functional effects. At the patient's first clinical visit with our plastic surgery team in 1989, we offered radical surgical resection of the mass, which was the standard of practice at the time. He declined radical resection. We have followed the patient clinically for over 26 years. Since presentation, the mass has not metastasized or caused any local functional problems.
Case:
We describe the case of a dysplasia epiphysealis hemimelica (DEH) lesion affecting uniquely the lunate bone in a 16-year-old boy causing pain, stiffness, and decreased range of motion. Surgical excision was performed, leading to resolution of primary symptoms with residual limitations in terminal wrist extension.
Conclusions:
From our review of the literature, we believe this case to be the first report of a DEH lesion affecting solely the lunate bone. Although conservative and surgical management have both been described with DEH cases, we report a positive outcome following the excision of a symptomatic lesion.
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