The infant had an extrathoracic heart covered only by visceral pericardium (complete thoracic ectopia cordis).The sternum was completely splitted with an inter-ridge distance of 5-6 cm, through which the heart was protruding for 4-5 cm and the apex pointing anteriorly.Since her birth, her activities are normal in relation to any other newborn infants including breast feeding, hands and feet movements etc. Her urinary and bowel systems were functioning normal.Initially her heart was covered with saline-soaked gauze pads& systemic antibiotics were given.Direct echocardiography showed single ventricle, grade-111 tricuspid regurgitation with severe pulmonary arterial hypertension (PASP-78).On her 3 rd day of birth at the National Institute of Cardiovascular Diseases, there was bleeding from her visceral pericardium for 5 minutes and she lost approximately 200ml of blood.After 15 days again bleeding occurred followed by a loud scream and cry in the beginning but this time bleeding lasted for 15 minutes and loss of around 400ml of blood. After her blood loss she became very weak and pale. Nutritional support was given by parenteral nutrition.Her complete blood count showed normal at that time. After 1 hour she was haemodynamically stable and began to intake breast milk of a very low quantity. She resumed her normal activities like before after a total of 6 hours approximately.Her parents were poor & her condition was very critical. Unfortunately the baby died on her 20 th days of birth. Ectopia Cordis Abstract:Ectopia cordisis characterized by partial or complete displacement of the heart out of the thoracic cavity The defect is a rare congenital abnormality, occurring in 5.5 to 7.9 per 1 million live births. 1 CASE REPORTS
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