Primary intraosseous carcinoma (PIOC), NOS is a rare malignancy occurring in the jaw bones. It may arise de novo, or more commonly develop from pre-existing lesions such as odontogenic cysts or tumours. In this manuscript, we describe a case of PIOC in the mandible of a 17year-old male. Complicating factors were a history of familial hemophagocytic lymphohistiocytosis and Griscelli syndrome. Management included surgical removal and planned adjuvant chemoradiation. The relevant literature is reviewed with respect to PIOC in a paediatric population.
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.