X-Linked sensorineuronal hearing loss (SNHL) is a rare but recognized cause of bilateral SNHL associated with CSF gusher. We report a case presenting a varied imaging spectrum and clinical scenario of a one year old boy with unilateral profound hearing loss and recurrent meningitis due to spontaneous oval window gusher. Imaging showed a unilateral abnormality, with the fistula leaking from the oval window into the middle ear cleft.
Introduction: Primary malignant scapular tumors are very rare. Little is written about flat bone sarcomas in the literature, and not much is known about the oncological outcome. Objective: The aim of the current work is reviewing clinicopathological features and surgical management of cases with primary malignant scapular tumors. Patients and methods: Patients with primary malignant scapular tumours who visited the National Cancer Institute (NCI) at Cairo University, Egypt, between January 2009 and December 2019 were subjected to a retrospective descriptive analysis. Results:The study included 25 patients with a mean age of 33.4 years old ranging from 9 to 86 years. Pathology types were chondrosarcoma in 14 patients (56%), Ewing/PNET in 7 patients (28%), osteosarcoma in 2 patients (8%), spindle cell sarcoma in 1 patient (4%), and aneurysmal bone cyst in 1 patient (4%). Twenty patients (80%) had surgery, and 5 patients (20%) had no surgical intervention for being either with a poor general condition or having metastatic disease. Overall survival at 6 months was 92% and was 88%, 75.4%, and 65.4% in the first year, 3 rd year, and 5 th year respectively. Disease-free survival at 6 months was 90.5%; and was 85.7%, 75.4%, and 42.7% in the first year, 3rd year, and 5th year respectively. Conclusion: Primary malignant scapular tumors are rare. Early diagnosis is very important, as surgical excision with a wide negative margin (limb-sparing surgery) is the main line of treatment in most cases and tends to decrease the recurrence rate, otherwise, palliative treatment and forequarter amputation may be indicated.
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.
hi@scite.ai
10624 S. Eastern Ave., Ste. A-614
Henderson, NV 89052, USA
Copyright © 2024 scite LLC. All rights reserved.
Made with 💙 for researchers
Part of the Research Solutions Family.