RESUMO -A síndrome de encefalite crônica com epilepsia (síndrome de Rasmussen) ocorre tipicamente em crianças e é caracterizada pelo desenvolvimento de epilepsia focal intratável, hemiparesia progressiva e deterioração intelectual. A etiologia é desconhecida e as anormalidades patológicas variam com a fase da doença. Relatamos o caso de um paciente jovem, com 17 anos de idade, com apresentação clínica da provável síndrome de Rasmussen. Discutimos a etiologia e o tratamento da patologia.PALAVRAS-CHAVE: síndrome de Rasmussen, epilepsia, tratamento clínico, imunoglobulina humana.
Probable Rasmussen's syndrome: case reportABSTRACT -The syndrome of chronic encephalitis with epilepsy (Rasmussen's syndrome) typically occurs in children and is characterized by the development of intractable focal seizures, progressive hemiparesis and intellectual deterioration. The etiology is unknown, and the pathological abnormalities vary. We report the case of a 17-year-old boy, presenting with clinical features typical of probable Rasmussen's syndrome. We discuss the etiology and treatment for this pathology.
RESUMO -Descrevemos dois casos clínicos de paraparesia espástica tropical / mielopatia associada ao HTLV-I (PET/MAH), segundo os critérios da OMS-1989. Estes são os primeiros casos diagnosticados em Florianópolis (SC-Brasil). Em um dos casos houve resposta clínica ao uso de metilprednisolona.PALAVRAS-CHAVE: paraparesia espástica tropical, HTLV-1, diagnóstico, metilprednisolona.
HTLV-I associated myelopathy/ tropical spastic paraparesis: report of two cases diagnosed in Florianópolis, Santa Catarina -BrazilABSTRACT -We describe two cases of tropical spastic paraparesis / HTLV-1 associated myelopathy, according to the criteria of World Health Organization-1989. These are the first cases diagnosed in Florianópolis (Santa Catarina State -Brazil). One of them had a good response with the treatment with methylprednisolone.
Two cases of partial Klüver-Bucy syndrome developed after probable herpes simplex meningoencephalitis are reported. Clinical, pathological, diagnostic and therapeutic aspects of herpes simplex encephalitis and Klüver-Bucy syndrome are discussed.
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