Although bowel function deteriorates with increasing age after operated HD, it is associated with only slightly decreased gastrointestinal quality of life.

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In children under 1 year of age, Hirschprung's disease is very unlikely in the presence of a RAIR. The specificity and positive predictive value of ARM for the diagnosis of Hirschprung's disease are inferior to those of rectal suction biopsy, and therefore, it cannot be recommended for use as a sole diagnostic tool for this disease. ARM may be a useful investigation in patients where the histologic specimen is inadequate and/or functional constipation is the most likely diagnosis. If RAIR is present, rectal biopsy may not be required.

Tumors of the small intestine are rare, constituting <5% of all gastrointestinal neoplasms (1). Gastrointestinal hemangiomas account for only 0.05% of all intestinal neoplasms (2). Patients with gastrointestinal hemangiomatosis can present with abdominal pain, intermittent bleeding, and anemia of varying severity, and sometimes obstruction or intussusception (2). Small-bowel hemangiomatosisusuallyisdifficulttodiagnosebecauseofitsrelative rarity and the fact that the workup for gastrointestinal bleeding is initially focused on the stomach, duodenum, and colon. We present a rare case of a 3-month-old female with extensive infantile hemangiomatosis affecting two thirds of the small bowel managed medically with thalidomide and somatostatin analog bitherapy.

No abstract