Ebstein anomaly is a rare pathology among congenital cardiac diseases with a prevalance of 0.5%. Ebstein anomaly patients suffer from arrhytmia, severe right ventricular dysfunction and left ventricular dysfunction due to cyanosis and right ventricular involvement. Most of the patients are presented at infancy, childhood and rarely after adolescence ages. Biventricular repair has a high mortality and morbidity and unacceptable func- tional results in Ebstein anomaly patients with severe right ventricular dysfunction, one and a half ventricle repair yields better results. In our case, we presented a one and a half ventricle repair with a successful Cone type repair in a 34-year-old male patient who referred to our clinic with cardiac arrest presentation and was detected to have functional type C Ebstein anomaly.
Holt-Oram syndrome is a disease with autosomal dominant inheritance characterized with cardiac defects and upper extremity skeletal anomalies. The prevalence of this syndrome is reported as 1 in 100.000 births. A 13-year-old female patient with Holt-Oram syndrome also called as Heart and Hand syndrome was presented. Tricuspid valve repairment was made in addition to the congenital cardiac defect repairment in the patient who also had tricuspid valve deficiency. The patient underwent a successful surgery.
Aortic arch anomalies are not clinically important unless they cause compression symptoms due to aneurysmatic dilatation. Aortic anomalies need to be treated when they cause complex thoracic aortic diseases, and the treatment approach has evolved over time from open surgical methods, which have high mortality and morbidity rates, to hybrid methods. A case of a 68-year-old male patient with complex aortic arch anomaly treated with hybrid arch repair is reported in this study. Aortic branches were common carotid trunk and aberrant right subclavian artery with a saccular aneurysm.
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