We present a case of a soft tissue chondroma arising in the neck of a 5-year-old girl with a 9-month history of respiratory distress and a slowly enlarging right neck mass of uncertain duration. The radiographic, sonographic, and CT features of this lesion will be discussed. This case is unusual due to the relatively rare nature of this lesion, its location, and its occurrence in a young child. This report also emphasizes the need to fully evaluate children with respiratory distress who do not respond to standard medical therapy.