SummaryA 25-year-old woman with chronic neuropsychiatric symptoms, peripheral neuropathy and hypoglycaemia was found to have an islet cell adenoma in the pancreas. Her neuropsychiatric symptoms disappeared following its removal and she partially recovered from her peripheral neuropathy.

Summary Medullary sponge kidney associated with a defect in urine acidification is rare and usually of no clinical significance. We report a case presenting as hypokalaemic paralysis due to associated congenital distal renal tubular acidosis.

This report presents a rare case of multiple accessory tragi, which developed at an unusual site outside of a derivative of a branchial arch, in this case the nose. Thus far, to our knowledge this is the 4 th reported case ofsimilar nature in the world. This case is significantin that, this is the first reported case with an accessory tragus present along the midline in the dorsum of the nose.