Introduction: Melanocytic neuroectodermal tumor of infancy (MNTI) is an uncommon pigmented neoplasm of neural crest origin, occurs mainly in the head and neck region specially maxilla. It shows slight male predominance . Melanocytic neuroectodermal tumor (MNTI) of testis is rare, proper diagnosis and differentiation from small round cells tumours (SRCT) is important as treatment modalities of these tumors are quite different.Case report: Here we present a case of MNTI of testis in an eleven month old male which was clinically diagnosed as teratoma. A distinctive morphology and immunohistochemistry play important role in postoperative diagnosis of this tumor. Conclusion:Treatment of MNTI is surgical excision with clear margins and follow up.

No abstract