We present a 67-year-old women with subacute onset of corticobasal-, partial Balint syndrome and exaggerated startle response as the presenting symptoms of Creutzfeld-Jakob disease (CJD). The previous 3 months she complained of a non-specific dizziness. Since 2 weeks she had trouble with using the coffee machine and dressing. Last week she started bumping into obstacles on her left side. Also, she seemed to ignore the food on the left side of her platter. Her left hand made "strange" unpurposeful movements.At admission, the patient was bradyphrenic and disoriented in time. Vital parameters were normal. There was apraxia with imitation (see video 1 ) and left-sided visual-and sensory extinction. We saw uncontrolled slow posturing movements of her left arm and hand as well as "arm levitation" (see video 1), which we interpreted as "alien limb phenomenon". Overall, movements were hypo-and bradykinetic and there was slight left-sided rigidity. The left leg displayed action-myoclonus (see video 2 ). FIG. 1. MRI showing cortical ribboning in right parieto-occipital region on DWI. FIG. 2. MRI showing cortical ribboning in right parieto-occipital region on ADC.
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