Pulmonary artery aneurysm (PAA) is defined as a main pulmonary artery (PA) diameter greater than 40 mm. Pulmonary arterial hypertension (PAH) is one of the conditions most commonly associated with the development of PAA but it is still uncertain which factors contribute to the development of PAA in PAH patients. We sought to identify the prevalence of PAA in PAH patients and to determine prognostic implications of PAA identification. METHODS: Data collection of patients in the Pulmonary Hypertension clinic at Keck Medical Center from January 2010 to January 2020 was conducted. Patient demographics and PAH etiology information was collected. Additional data regarding functional status, as determined by NYHA class and 6 MWD, and hemodynamics per RHC and TTE measurements was collected. Patients were described as having Pulmonary Artery Aneurysms if their CT report noted a main PA size greater than or equal to 40 mm.
Pulmonary artery aneurysm (PAA) is defined as a main pulmonary artery (PA) diameter greater than 40 mm. It is seen in up to 20% of patients with Pulmonary Arterial Hypertension (PAH). Uncertainty remains regarding the predictive factors for the development of PAA in PAH patients as well as the characteristics of this subgroup of patients. We describe a retrospective cohort of patients to help address these knowledge gaps.
Pulmonary hypertension is a highly heterogeneous condition with multiple etiologies.The World Health Organization (WHO) classifies patients into five groups based on the etiology. Group 1 pulmonary hypertension is referred to as pulmonary arterial hypertension (PAH). This umbrella category contains many subgroups. We present our center's experience and our cohort of WHO Group 1 PAH and its subgroups in comparison to Reveal Registry.
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