Adenomatoid odontogenic tumours are hamartomatous lesions that rarely deviate from their well-recognised radiological features. However, increasing numbers with atypical radiological features have been reported in recent years. This study reports on a large extrafollicular lesion in the anterior mandible with uncommon radiological features in a 17-year-old female. Treatment included enucleation with a histopathological confirmation. Healing was uneventful. Statement of clinical relevanceThe current lesion depicted atypical radiological features. Distinctive radiological features may not always be apparent in conventional radiographs. Hence, the use of advanced imaging may improve radiographic interpretation in differentiating from radiographically similar appearing lesions.

Aim: This article describes the craniofacial and dental features of an individual with Gordon syndrome. The dental management implications and considerations of treating patients with Gordon Syndrome and similar conditions resulting in limited mouth opening are discussed. Methods: A 14-year-old South African male was referred to the Dental Genetics Clinic with the main complaint of carious teeth. His craniofacial characteristics included low set and posteriorly rotated ears, down-slanted palpebral fissures, sloping shoulders, and a broad neck. A prognathic mandible and mild facial asymmetry were noted. He had a significant limitation of mouth opening (2 cm at incisors). Radiographic examination revealed multiple carious teeth, missing mandibular premolars, impacted maxillary premolars, taurodontism of the 44 and 34, and enlarged coronoid processes of the mandible. Dental extractions and restorations have been performed under local anaesthesia. Conclusion: Gordon syndrome and similar conditions, may result in limited oral opening and impaired manual dexterity. The severity of limitation of mouth opening determines management. Dental management should focus on ensuring that the patient is able to maintain good oral hygiene by customising homecare for the individual and regular dental visits. K E Y W O R D Sdistal arthrogryposis, Gordon syndrome, limited mouth opening BACKGROUNDGordon syndrome (OMIM 114300), also known as Distal Arthrogryposis type 3, is a rare autosomal-dominant genetic disorder. 1,2 It falls within the spectrum of conditions known as Arthrogryposis Multiplex Congenita (AMC) which is used to describe congenital arthrogryposis affecting two or more areas of the body. The condition was first described by Gordon et al in 1969, in a South African family consisting of six affected individuals over three generations. 2 The condition is characterised by

A 9-year-old female presented with a history of a firm painless bony swelling at the left mandible. A pantomograph (Figure 1) revealed a large radiopaque mass in the mandibular body with impaction of the 36. What are the most distinguishing radiological features and what is your provisional diagnosis?

This 10-year-old boy presented with a main complaint of a carious painful primary molar in the third quadrant. A pantomograph revealed an incidental mass in the right posterior maxilla (Figure 1). No other symptoms were reported. What are the most important radiological features and what is your provisional diagnosis?

A bulging swelling was observed in the anterior maxilla that resulted in displacement of nasal features and enlargement of the right nostril. Adjacent teeth tested vital and the contents radiodensity measured approximately 22 Hounsfield units (HU) on CT imaging