We present case series of four patients with an important syndrome known as Herlyn-Werner-Wunderlich syndrome. Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos. Awareness is necessary to diagnose and treat this disorder properly before complications occur. Magnetic resonance imaging is the preferred modality for the delineation of uterine malformation. When renal anomalies are encountered, a screening should also be made for congenital abnormalities of the reproductive tract and vice versa.
A 32-year old primigravida female of approximately 20 weeks gestation by her last menstrual period (spontaneous conception) was referred for anomaly scan. The ultrasonography revealed two uterine horns separated by thick (12 mm) uterine tissue with a fetus (average Gestational age 22 weeks each) in each horn.
Unicornuate uterus with a non-communicating horn is a rare anomaly and even rarer pregnancy in its noncommunicating horn. The incidence of pregnancy in the non-communicating horn is 1 in 76,000 to 1 in 150,000. Due to non-compliant uterine musculature in the noncommunicating horn, it is prone to rupture in cases of pregnancy. The rupture occurs usually in the second trimester. We describe a case which presented with the rupture of non-communicating horn with live fetus inside it. The present case had a 22 week fetus floating in the peritoneal cavity following the rupture of non-communicating horn with normal other uterine horn.
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