Non-compaction cardiomyopathy (NCC) is characterized by trabeculations in either one or both ventricles. Clinical presentation is highly variable: dyspnea, palpitation, thromboembolic events, arrhythmia, or sudden cardiac death. There are currently no universally-accepted criteria for classifying and diagnosing left ventricular non-compaction (LVNC) cardiomyopathy. Transthoracic echocardiography (TTE) is the diagnostic exam of choice. The diagnosis is often missed or delayed because of a lack of knowledge about this uncommon disease. Progression of LVNC is highly variable and prognosis is very difficult to predict.
We report a case of a 50-year-old female patient with a history of total thyroidectomy under hormonal supplementation who consults for dyspnea and paroxysmal palpitations revealing an isolated LVNC.
This case emphasizes the importance of imaging techniques, which are, TTE and cardiac magnetic resonance imaging (MRI) in early diagnosis, management, and follow-up.
Vasospastic angina (VA), is characterized by symptoms of coronary angina caused by coronary vasospasm, usually in the absence of atherosclerotic changes. It typically presents with chest pain, which can be accompanied by transient electrocardiographic changes, if visualized during the attack. It can also rarely present with severe manifestations of acute myocardial angina, ventricular tachycardia (VT), ventricular fibrillation or cardiac arrest. We report the case of a 25-year-old male patient, with cannabis smoking habit, admitted for palpitations which had revealed a VT in the electrocardiogram (ECG), and for whom a coronary angiography was realised showing a coronary artery spasm (CAS) with no sign of atherosclerotic occlusion.
Schönlein-Henoch purpura is a non-thrombocytopenic systemic vasculitis of small-caliber vessels due to immune complexes. We report the case of an adult 30 year old man admitted for a generalized edematous syndrome with purpuric lesions in the 2 lower limbs revealing a dilated cardiomyopathy whose etiological assessment was in favor of a Schönlein-Henoch purpura with cardiac, renal, dermatological involvement. The diagnosis was difficult to establish given the clinical polymorphism. Also, management was complicated given the multifocal involvement. The treatment was based on corticosteroid therapy and rituximab but the evolution was, unfortunately, not satisfactory.
Erdheim-Chester disease (ECD) is a rare non-Langerhans histiocytic multisystem disorder due to xanthogranulomatous infiltration of tissues by spumous histiocytes, It typically presents with diffuse bone pain however the cardiac manifestation are common and occur to 75% of the patients. It is frequently asymptomatic and detected incidentally on radiological imaging and it most commonly manifests as pericardium and myocardium infiltration We report the case of a 66-year-old woman patient, admitted for diffuse bone pain, asthenia and a left arm weakness who presented and infiltration of the aorta with a coated aspect, a thickened right atrium and a small pericardial effusion.
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