Background
Low-grade fibromyxoid sarcoma (LGFMS) is an uncommon neoplasm generally affecting muscle tissue. It presents rarely in abdominal viscera and even more rarely occurs in the pancreas. All types of pancreatic sarcomas are uncommon, and LGFMS is a rarer still. We present the case of an LGFMS in the pancreas. Because of its rarity, there are no guidelines for appropriate treatment or summations of the natural course of this illness.
Case presentation
We present the case of a 49-year-old female who presented with epigastric pain. She had a prior history of three episodes of acute pancreatitis many years earlier. A CT revealed a pancreatic body mass, which was biopsied. Pathology returned LGFMS. The patient underwent a distal pancreatectomy and splenectomy. She did well after the case and did not require further intervention.
Conclusion
Though it is exceedingly rare, cases of pancreatic LGFMS should be reported in order to guide clinical decisions. LGFMS has been shown to have high malignant potential in other tissues, and there is no reason to think pancreatic masses will be different. By building a body of evidence about these rare tumors, patient care will benefit.
Low Grade Fibromyxoid Sarcoma (LGFMS) is an uncommon neoplasm generally
affecting muscle tissue. It presents rarely in abdominal viscera and
even more rarely occurs in the pancreas. We present the case of a
49-year-old female who underwent a distal pancreatectomy and splenectomy
for a LGFMS causing epigastric pain.
Renal nutcracker syndrome ia a rare cause of chronic pain and hematuria.
A literature search was conducted through PubMed. Forty studies and our
own series were included in the review, for a total of 73 individual
patient cases. NCS is an uncommon cause of hematuria, flank pain,
abdominal symptoms
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