No abstract

No abstract

A 56 year old woman with acute intermittent porphyria presented mainly motor polyneuropathy, ophthalmoparesis of probable supranuclear origin and a mild organic brain syndrome. The neurological complications gradually cleared during a course of plasmapheresis. The fairly rapid improvement could conceivably have been fortuitous but it may well have been due to plasmapheresis.

A prevalence study of Huntington's chorea in Florence area in the period 1970-1979. Two clusters have been identified and the frequency of subjects heterozygote for Huntington's gene has been determined for planning Public Health intervention and the preparation of correct genetic counselling.

A marked rim of contrast uptake in the subarachnoid spaces at the level of the tentorium on CT scanning was a bit of a riddle. When correctly interpreted, the finding, in agreement with the clinical and CSF findings, led to the diagnosis of tuberculous meningitis in a 72 year old woman. The case is reported to further the correct assessment of the CT image in this disease.