Diaphragmatic hernia is an important cause of emergency hospital admission associated with significant morbidity. It usually results from congenital defect or rupture in the diaphragm due to trauma. Prompt and appropriate diagnosis is necessary in patients with this condition, as surgical intervention by either abdominal or thoracic approach may be necessary. Here, we report a case of left-sided diaphragmatic hernia presenting with sudden onset of breathlessness, respiratory distress and left-sided chest pain radiating to the abdomen, mimicking pneumothorax, treated successfully with surgical intervention.
Background: Pseudomyxoma peritonei with disseminated peritoneal adenomucinosis is a rare, chronic, relapsing, diagnostically challenging and poorly understood disease characterized by mucinous ascites and peritoneal implants.Methods: All the patients diagnosed as pseudomyxoma peritoneii admitted to Amrita Institute of Medical Sciences were analysed retrospectively. A total of 17 patients were analysed with regard to sex, mode of presentation, management, histopathological analysis and further treatment. Patients with peritoneal implants that came positive for malignancy were excluded from the study.Results: 17 patients were studied; out of which, majority were females 64.7% (11), abdominal distension 52.9% (9) was the most common presentation, 52.9% (9) patients underwent cytoreductive that was thought to be incomplete, 47.05% (8) had complete cytoreductive surgery. In 94.11% ( 16), the origin of majority of the tumors were appendix with only case where the origin was from ovary and appendix was found to be normal. Histopathologically, 29.4% (5) was mucinous cystadenoma of appendix with DPAM, 41.2% (7) cystadenocarcinoma of the appendix, 29.4% (5) patients were diagnosed as mucinous neoplasm of appendix with uncertain malignant potential with disseminated peritoneal adenomucinosis (DPAM). Patients with malignant features in appendix were considered for adjuvant chemotherapy. Most of the patients were followed-up for a period ranging from 1 year to 7 years with a median of 3 years. Out of 17 patients, 5 patients developed features of recurrence but were managed conservatively without the need for surgery.Conclusion: Disseminated peritoneal adenomucinosis (DPAM) is a distinct clinical entity when peritoneal carcinomatosis is to be ruled out. Appendix is the most common origin of DPAM even in females. Abdominal distension is the commonest presentation. Surgical debulking is an ideal option even when complete cytoreductive surgery is not possible. Assessment of tumor histology is important in ruling out the peritoneal carcinoma. In DPAM, good long-term results can be obtained with only cytoreductive surgery.
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.
customersupport@researchsolutions.com
10624 S. Eastern Ave., Ste. A-614
Henderson, NV 89052, USA
Copyright © 2024 scite LLC. All rights reserved.
Made with 💙 for researchers
Part of the Research Solutions Family.