the forehead and orbital dystopia, the most common underlying cause being usually an unilateral coronal suture synostosis. Differential diagnoses done mainly with anterior deformational asymmetries [1]. However, frontal craniosynostosis could be related to isolated involvement of other components of the coronal ring such as frontosphenoidal suture [2]. In 1995, Francel and collegues reported the first case of isolated frontosphenoidal craniosynostosis [3] and so far, only isolated case reports [2,4-18] and small retrospective studies have been published in the literature [19,20]. Both forms of monosutural craniosynostosis -coronal and frontosphenoidal -may lead to a similar but subtly distinct phenotype and radiological presentation. Therefore, it is capital to differentiate these entities to select the most appropriate surgical correction. We report three patients with a diagnosis of frontosphenoidal craniosynostosis and compare them with the more frequent: coronal craniosynostosis. The aim of this paper is to describe and identify the differences between the two craniofacial deformities and to detail the surgical procedures to correct them. Case Descriptions Case 1A 8-months-old first born boy was referred to our Department due to frontal asymmetry. Antenatal history was unremarkable and delivery was uncomplicated. A progressive flattening of the left forehead was observed by his parents at the age of 5-6 months. After consultation with his primary care pediatrician,