Ectopia cordis (EC) is a rare malformation due to failure of maturation of the midline mesodermal components of the chest and abdomen. It can be defined as 0.1% of congenital heart diseases, and it could present isolated or could belong to the spectrum of the Pentalogy of Cantrell (PoC), which is a rare congenital disorder first described in 1958 by Cantrell. We are reporting a rare case of total ectopia cordis, associated to a major omphalocele, total agenesis of the sternum, anterior diaphragmatic deficiency, absence of pericardium, and persistence of the Ductus arteriosus, making therefore these features compatible with a full spectrum of the Pentalogy of Cantrell, encouraging us to report this case.Key words: Ectopia cordis, major omphalocele, sternum agenesis, anterior diaphragmatic deficiency, absence of pericardium, persistence of the Ductus arteriosus.
Hydatid disease is one of the important health problems in developing countries. Can affect any part of the human body, it commonly affects lungs and liver. Because of poor data and preventive measures in Sub-Saharan Africa, cystic echinococcosis (CE) is regarded as endemic disease. This is a retrospective study of children ages of 3 to 12 years admitted in pediatric surgical unit at Nelson Mandela Academic Hospital (NMAH), from April 2015 to aril 2020. We studied groups of age, sex, organs affected, treatment and complications. We studied 56 children; the group of age most affected was 5 to 10 years, females accounted for 51.8%, and male for 48.2%, lung hydatid cysts in 44.6% of cases, 41.1% had liver cysts, 8.9% of the patients had cysts in multiple locations. In 46 cases (82%), the treatment was surgical: punction-aspiration-injection and respiration (PAIR) removing the germinal layer, following in the post operatory with Albendazole and Praziquantel. In 10 cases (18//%) was given only medical treatment. Females were most affected, and the lungs were the organs most affected followed by liver.
Hydatid infestation of the lung can be primary or secondary. Cystic echinococcosis (CE) is regarded as endemic in Sub-Saharan Africa, however, for most countries only scarce data, if any, exist. This is a retrospective analysis of children below 13 years with lung hydatid cyst admitted in the paediatric surgical ward at NMAH (Nelson Mandela Academic Hospital) in Eastern Cape, South Africa. The study period was from September 2015 to September 2017. The variables studied were age, sex, imagen findings, cysts sizes, treatment and complications. Prevalence and behaviour of lung hydatic cyst in our children were found out. There were 12 children studied, 8 females and 4 males. The age ranges from 5 to 10 years. The 50% of the children were to 10 years. The left lung was more affected, 7 patients constituting 58.3%, bilateral disease was seen in 3 patients. Treatment was surgical: punction, aspiration, injection and reaspiration (PAIR), removal of germinal layer, and partial capitonnage on a drain tube in 8 children (67%). A pharmacological treatment was offered to 4 patients. There was rupture of a cyst into the pleural space before surgery. Postoperatively 7 children developed broncho-pleural fistula. There was no mortality in this study. Hydatid cyst of the lung was most frequent on the left side. The surgical treatment performed was PAIR mostly in cysts more than 6 cm or with complications. Conservative treatment is an option in some cases.
Intr can affect any sub-Saharan A and the organs between the a Eastern Cape, was to assess w the group of a lung cysts, 46% and 2% hamst (PAIR) remov required medi affected than m
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.
hi@scite.ai
10624 S. Eastern Ave., Ste. A-614
Henderson, NV 89052, USA
Copyright © 2024 scite LLC. All rights reserved.
Made with 💙 for researchers
Part of the Research Solutions Family.