Highlights
Mucinous adenocarcinoma of the perianal region is extremely rare (6.9% of anal neoplasms and 2–3% of all gastrointestinal malignancies).
Given the low incidence of this tumor, it is often missed at initial evaluation.
Association with chronic perianal fistula are common and inflammatory symptoms can be misleading with delay in diagnosis.
The paucity of publications leads to a lack of consensus on both diagnostic and therapeutic approaches.
The understanding of the etiopathogenic mechanisms may lead to the development of novel diagnostic and therapeutic protocols.
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.