Objective:To describe a case of hearing rehabilitation with bone anchored hearing aid in a
patient with Treacher Collins syndrome.Case description:3 years old patient, male, with Treacher Collins syndrome and severe complications
due to the syndrome, mostly related to the upper airway and hearing. He had
bilateral atresia of external auditory canals, and malformation of the pinna. The
initial hearing rehabilitation was with bone vibration arch, but there was poor
acceptance due the discomfort caused by skull compression. It was prescribed a
model of bone-anchored hearing aid, in soft band format. The results were
evaluated through behavioral hearing tests and questionnaires Meaningful Use of
Speech Scale (MUSS) and Infant-Toddler Meaningful Auditory Integration Scale
(IT-MAIS).Comments:The patient had a higher acceptance of the bone-anchored hearing aid compared to
the traditional bone vibration arch. Audiological tests and the speech and
auditory skills assessments also showed better communication and hearing outcomes.
The bone-anchored hearing aid is a good option in hearing rehabilitation in this
syndrome.
scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.