Les malformations kystiques des voies biliaires sont des affections congénitales rares évaluées à environ 1/2 000 000 naissances. C'est une affection qui peut se révéler gravement par une complication notamment l'angiocholite, la pancréatite chronique, cirrhose biliaire progressive, l'hypertension portale ou les lithiases biliaires. Sa perforation spontanée est l'une des rares complications, décrite pour la première fois en 1934 par Weber. Nous rapportant le cas d'un garçon de 18 mois admis pour syndrome sub-occlusif avec une péritonite biliaire. Une échographie a été réalisée montrant un épanchement abdominal avec formation kystique communicante des voies biliaires associée à un épanchement sous capsulaire du foie confirmé par scanner. L'intervention a consisté en une toilette péritonéale avec mise en place d'un drain de redon au niveau de la perforation et un drain sous hépatique sans excision du kyste. Le patient a été réadmis 6 mois après cet incident pour sa cure définitive.
Ovarian sex cord tumors are rare tumors that develop at the expense of non-germ cell ovarian. The pathogenesis of these tumors remains undetermined and several cellular and molecular alterations may be involved in the development of juvenile granulosa cell tumors. For two decades, the individualization of juvenile granulosa cell tumors has been a major advance in the treatment of these children's tumors. However, their natural history is reported in the literature and through a short series and reliable prognostic factors are to establish. We report the case of a girl of 8 years who presented with abdominal-pelvic mass gradually increasing size, to surgical exploration found a huge abdominal mass at the expense of the left ovary. Histology and objective immunolabeling a tumor of the juvenile form of granulosa.
An 8-year-old girl with no particular pathological history, had been suffering for about 15 days from pelvic pain, paroxysmal, of moderate intensity, associated with an increase in abdominal volume and unquantifi ed weight loss. The abdominal examination found a painless abdominalpelvic mass measuring approximately 25 ×20 cm in diameter, of hard consistency, poorly limited, mobile with respect to the superfi cial plane, and fi xed with respect to the deep plane, with collateral venous circulation, without signs of hypersecretion and an undeplested umbilicus. The abdominal-pelvic ultrasound was performed, it revealed a large abdominalpelvic mass, occupying almost the totality of the abdomen, compatible with a supravesical cystic mass (Figure 1), associated with an intraperitoneal effusion of low abundance, without deep adenopathy, and without hepatic involvement. An abdominal-pelvic Computed Tomography (CT) scan objectifi ed a multicompartmentalized cystic mass, supraabdominal and left latero-vesical, which may correspond to a
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