“…(6) Presence of degenerative stigmata (cryptorchismus, adherent lobules of the ear, facial asymmetry, congenital cataract). (7) In two cases there was some weakness of the extrinsic eye muscles. Behr looked upon his cases as representing a transition type (Unterart) between Leber's disease and Striimpell's spastic paralysis on the one hand and the heredo-ataxias on the other.…”