Word List Learning in Patients with Polycystic Lipomembranous Osteodysplasia with Sclerosing Leukoencephalopathy

Vanhanen, Matti; Hakola, Panu; Ilonen, Tuula; Tiihonen, Jari

doi:10.1159/000346857

Cited by 1 publication

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“…These both symptoms have been described in casu in the monographs of Hakola (1,4). The deterioration of visual memory has been published separately (23) as well as the defect of verbal memory (24). The test pattern used by Hakola in his follow-up studies contained the Rorschach test also to assess personality functioning of these patients.…”

Section: Introductionmentioning

confidence: 99%

Rorschach assessment of personality functioning in patients with polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy

Ilonen

Hakola

Vanhanen

et al. 2012

Acta Neuropsychiatr.

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Ilonen T, Hakola P, Vanhanen M, Tiihonen J. Rorschach assessment of personality functioning in patients with polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy. Objective:To date no studies have investigated the personality functioning underlying patients diagnosed with polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy (PLOSL) using the performance-based Rorschach test. Methods: We scored and interpreted the Rorschach protocols of eight carefully diagnosed PLOSL patients according to Exner's Comprehensive System. The structural variables in the Rorschach are organised around the seven dimensions of personality functioning that they assess: coping style and resources, organising information, perceiving events, forming concepts and ideas, handling of emotions, self-perception and interpersonal perception. Results: As a group PLOSL patients had many personality liabilities when contrasted with typical avoidant non-patient adults. A majority of patients showed an avoidant coping style (Lambda > 0.99), low productivity and poor verbal output in the low number of responses and few Blends. Also, they showed limited available resources to cope with problem-solving test. Problems in organising information efficiently, and perceiving events realistically as well as signs of disturbed thinking and concept formation were observed in many patients. Handling of emotions was characterised by avoidance of emotional stimuli but at the same time poor affect modulation. Capacities to view themselves and others were thoroughly limited. Conclusions: PLOSL tends to have repercussions throughout the personality functioning. In line with clinical findings and later neuroradiological and neuropathological examinations the Rorschach revealed personality features typical for frontal type of dementia. Significant outcomes• PLOSL, which is a rare fatal disease affecting nervous and musculoskeletal systems, also deeply affects personality. • Polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy (PLOSL) patients show similar personality features to those typical for frontal type of dementia. • The Rorschach, as a perceptual-cognitive problem-solving test, is suitable also for patients who are neurologically impaired. Personality in PLOSL patients Limitations• The data were collected mostly in third and fourth illness phases, thus we do not know the primary personality functioning of these patients. • We were able to analyse only a part of the collected data because those in the most severe disease phase were not able to produce valid Rorschach protocols. • Small sample size caused problems for statistical analysis.

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Section: Introductionmentioning

confidence: 99%