Woolly Hair Nevus Type I

Abstract

ABSTRACT:Woolly hair nevus is a very rare non hereditary disorder of scalp. It is characterized by presence of one or more circumscribed regions of curly/ kinky, smooth, shiny hair of woolly texture, generally of the lighter color than the normal hair over scalp. In over half of the reported cases, a pigmented or epidermal nevus has been present, but not always at the same site. Its onset is usually within first years of life. We present a case of woolly hair nevus type I with no associated abnormalities, which is quiet rare. KEYWORDS: Woolly hair, woolly hair nevus, curly hair. INTRODUCTION:Woolly hair is normal in negroids. However, in non-negroid, it is a hereditary anomaly of the hair. The woolly hair nevus is very rare non-hereditary disorder of the scalp. It is characterized by presence of one or more circumscribed regions of curly/ kinky, smooth, shiny hair of woolly texture, generally of the lighter color than the normal hair over scalp. 1 The remaining hair on the scalp exhibit no peculiarities. In over half of the reported cases, a pigmented or epidermal nevus has been present, but not always at the same site. 2 We present a case of woolly hair nevus type I with no associated anomalies, which is quiet a rare phenomenon.