Wilms' tumor in the horseshoe kidney

Pilocytic astrocytoma with leptomeningeal spread in a patient with incontinentia pigmenti presenting with unilateral nystagmus

“…early onset, uncharacteristic spread) is often seen with "tumor predisposition" and it is provocative in the context of other reported neoplasms in patients with IP. Three cases of Wilms tumor in the setting of IP have been reported, with one patient also developing a paratesticular rhabdomyosarcoma . One case of acute myeloid leukemia and two cases of retinoblastoma, one bilateral, have been described in association with IP .…”

“…Three cases of Wilms tumor in the setting of IP have been reported, with one patient also developing a paratesticular rhabdomyosarcoma. [8][9][10] One case of acute myeloid leukemia and two cases of retinoblastoma, one bilateral, have been described in association with IP. [11][12][13] There are multiple case reports of squamous cell carcinoma (SCC), 14,15 namely subungual SCC, 16…”

Wilms' tumor in horseshoe kidney: Presentation due to ureteropelvic junction obstruction

“…In addition, both ureters take unusual courses due to the abnormal position of the renal pelvis. Because of this, the ureter on the normal side is prone to inadvertent operative injury [22].…”

“…It has been suggested that any child with horseshoe kidney should undergo frequent periodic physical examinations to identify any Wilms' tumor that may arise [22]. Because of its position in the midline overlying the spine, a horseshoe kidney is readily accessible to physical examination and thus a tumor could be discovered at an early stage.…”

Fatty Wilms' tumor simulating teratoma; occurrence in a child with horseshoe kidney

“…An unusually fatty wilms' tumor occured in a young girl. Because of the abundant fat it radiologically simulated a teratoma.CT and ultrasound (US) studies suggested that the mass demonstrated within a horseshoe kidney was a teratoma rather than a Wilms' tumor.Wilms' tumor (WT) arises in horseshoe kidneys with greater frequency than in nonfused kidneys [1][2][3][4][5][6][7]. Review of children enrolled in the National Wilms' Tumor Study Group indicated that the risk of Wilms' tumor is approximately 2-8 times more than expected if there were no association [7].…”