What Lurks Beneath: Incidental Finding of a Pulmonary Artery Aneurysm Secondary to Pulmonary Valve Stenosis

Pulmonary Artery Aneurysm Repair with Alpha-1 Anti-trypsin Deficiency

“…1 There are few reports of isolated congenital pulmonic valve stenosis with associated pulmonary artery aneurysm, and no reports of open repair in a patient with Alpha-1 Antitrypsin deficiency. 2,3 We present a case of a patient with Alpha-1 Antitrypsin deficiency who presented with idiopathic congenital pulmonic valve stenosis, with findings of a pulmonary artery aneurysm, and successful open operative repair.…”