Vulvar syringoma: A rare cause of pruritus vulvae

Abstract

Syringomas commonly occur in women over the face, neck, and chest. They are usually asymptomatic and mainly of cosmetic concern. The vulva is an uncommon site for syringomas. A 45-year-old woman had asymptomatic lesions over the face, of 28 years duration and presented with vulvar papules, associated with severe pruritus for the past 2 months. Clinical and histopathological examination confirmed them to be syringomas. Coexistent facial and vulvar syringomas are rare. Further, vulvar syringomas presenting as pruritus vulvae is still rarer. We report a case with severe pruritus vulvae causing sufficient distress to seek medical care, which is remarkably unusual.

Vulvar syringomas — an underrecognized condition

“…An unequivocal diagnosis is made on histopathological examination, which shows a dermal proliferation composed of cells arranged in nests and channels with fibrous stroma. Some of these channels have characteristic small tails of comma-shaped epithelioid cells, resembling tadpoles [1]. An auxiliary non-invasive method is being sought to make a preliminary diagnosis.…”

“…Syringomas are benign neoplasms of the adnexa, most commonly presenting as multiple skin-coloured nodules located on the face, especially on the lower eyelids, neck, and trunk. Uncommonly, the occurrence of syringomas is limited to the vulva, without involvement of extra-genital locations [1].…”