“…The vulvar location is exceptional; 17 cases were found in the literature, including some of vulvar mastocytoma and vulvar swelling, but other cases (1-8) featured this particular multiple papulo-nodular clinical aspect, which requires a differential diagnosis with Langerhans histiocytosis (9) and other causes of vulvar papulo-nodules, such as pseudo-verrucous papules linked to local irritation, condylomas, molluscum contagiosum, xanthomas and juvenile xanthogranulomas (5,6).…”