Video/EEG aspects of early-infantile epileptic encephalopathy with suppression-bursts (Ohtahara syndrome)

Fusco, Lucia; Pachatz, Christa; Capua, M. Di; Vigevano, Federico

doi:10.1016/s0387-7604(01)00280-7

Cited by 43 publications

(36 citation statements)

References 7 publications

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“…This means that the EEG (electroencephalogram) tends to show periods of very little electrical brain activity followed by a burst of high spiky activity before returning to very low activity again. Sometimes, one side of the brain seems to be affected more than the other [5]. Seizures are intractable; although in some cases they can be improved through treatment.…”

Section: Epileptic Encephalopathy Syndromes In Infancymentioning

confidence: 99%

Epileptic Encephalopathies: An Overview

Khan

Baradie

2012

Epilepsy Research and Treatment

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Epileptic encephalopathies are an epileptic condition characterized by epileptiform abnormalities associated with progressive cerebral dysfunction. In the classification of the International League Against Epilepsy eight age-related epileptic encephalopathy syndromes are recognized. These syndromes include early myoclonic encephalopathy and Ohtahara syndrome in the neonatal period, West syndrome and Dravet syndrome in infancy, myoclonic status in nonprogressive encephalopathies, and Lennox-Gastaut syndrome, Landau-Kleffner syndrome, and epilepsy with continuous spike waves during slow wave sleep in childhood and adolescences. Other epileptic syndromes such as migrating partial seizures in infancy and severe epilepsy with multiple independent spike foci may be reasonably added. In this paper, we provide an overview of epileptic encephalopathies including clinical neurophysiological features, cognitive deterioration, and management options especially that these conditions are generally refractory to standard antiepileptic drugs.

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Section: Epileptic Encephalopathy Syndromes In Infancymentioning

confidence: 99%

Epileptic Encephalopathies: An Overview

Khan

Baradie

2012

Epilepsy Research and Treatment

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“…For those who survive, EEG wake-sleep differentiation occurs from 40 days to 5 months, with more apparent suppression burst in sleep [7]. During wakefulness, suppression burst pattern evolves into hypsarrhythmia pattern, diffuse slowing, multifocal abnormalities, or pseudoperiodic pattern with improved background organization [8].…”

Section: Neonatal/infantile Onset Epilepsy Syndromesmentioning

confidence: 99%

“…The burst activities of the suppression burst pattern coincide with tonic seizures [7]. Focal seizures may start as focal rhythmic spike and wave activity followed by tonic seizures.…”

Section: Neonatal/infantile Onset Epilepsy Syndromesmentioning

confidence: 99%

Electroencephalogram of Age-Dependent Epileptic Encephalopathies in Infancy and Early Childhood

Wong‐Kisiel

Nickels

2013

Epilepsy Research and Treatment

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Epileptic encephalopathy syndromes are disorders in which the epileptiform abnormalities are thought to contribute to a progressive cerebral dysfunction. Characteristic electroencephalogram findings have an important diagnostic value in classification of epileptic encephalopathy syndromes. In this paper, we focus on electroencephalogram findings of childhood epileptic encephalopathy syndromes and provide sample illustrations.

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“…This means the EEG (electroencephalogram) tends to show periods of very little electrical brain activity followed by a burst of high spiky activity before returning to very low activity again. Sometimes, one side of the brain seems to be affected more than the other (Fusco, 2001). -Seizures are intractable, although in some cases can be improved through with treatment (Komaki,1999).…”

Section: Symptoms -mentioning

confidence: 99%

Epileptic Encephalopathy Syndromes in Infancy

Albaradie¹

2011

Epilepsy in Children - Clinical and Social Aspects

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Video/EEG aspects of early-infantile epileptic encephalopathy with suppression-bursts (Ohtahara syndrome)

Cited by 43 publications

References 7 publications

Epileptic Encephalopathies: An Overview

Epileptic Encephalopathies: An Overview

Electroencephalogram of Age-Dependent Epileptic Encephalopathies in Infancy and Early Childhood

Epileptic Encephalopathy Syndromes in Infancy

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