Vascular Disease Associated With Angioid Streaks of the Retina and Pseudoxanthoma Elasticum

Vascular Abnormalities Associated with Pseudoxanthoma Elasticum

“…Four of his 15 patients had definite symptoms of intermittent claudication which had begun at the age of 18 in one case, at 36 in another and during the fifth decade in the remaining two. Intermittent claudication since childhood has been reported in a man with pseudoxanthoma elasticum and angioid streaks (Scheie and Freeman, 1946). When this patient was examined at the age of 26 no pulsation could be felt in either the dorsalis pedis or posterior tibial artery.…”

“…The altemative explanation is that there is some obliteration of the lumen and that the normal resting flow is the result of a well-developed anastomotic circulaion. Biopsy of a non-pulsatile ulnar artery in a case of the 86 Gronblad-Strandberg syndrome (Scheie and Freeman, 1946) suggests that both factors may play a part. The lumen of the vessel was found to be smaller than normal but it was not occluded.…”

Pseudoxanthoma elasticum: A review of neurological complications

“…Frequent association of prominent mental or psychiatric disturbances such as forgetfulness or impaired memory, dull mentality, depression [ 11, psychoneurosis [9], and mental deterioration [ 111 all have been described in association with PXE.…”

Pseudoxanthoma Elasticum

“…REPORT OF CASE D. T., a 75-year-old obese Cuban woman, with a moderately severe kyphoscoliosis, was first seen in the dermatology clinic of the University of Illinois Research and Education Hospital on June 16,1953. She demonstrated an asymptomatic lesion located on the abdomen which had been present for two years.…”