Uterus didelphys with unilateral obstructed hemivagina with hematometrocolpos and hematosalpinx with ipsilateral renal agenesis

Abstract

Uterus didelphys with blind hemivagina and ipsilateral renal agenesis (Herlyn Werner-Wunderlich Syndrome) is a rare congenital anomaly. It mostly presents with severe dysmenorrhea and a palpable mass due to unilateral hematocolpos. A patient with dysmenorrhea from a double uterus and an obstructed hemivagina is a diagnostic dilemma because the menses are regular. We report a case of a 14-year-old girl with this condition who was diagnosed as uterus didelphys with unilateral hematocolpos and hydrosalpinx with ipsilateral renal agenesis on the basis of sonography and confirmed by laparoscopic examination.

Sonographic diagnosis of Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: a report of two cases

“…, 9 , 10 , 17 , 20 This may be performed as a single‐stage or two‐stage procedure. The single stage procedure involves excising the vaginal septum completely and marsupialising the vaginal cuff.…”

Herlyn-Werner-Wunderlich syndrome complicated with pyocolpos: an unusual cause of postabortal sepsis

“…3 The triad has been described as HerlynWerner-Wunderlich syndrome. 4,5 More recently, the acronym OHVIRA is used to describe patients with obstructed hemivagina and ipsilateral renal anomaly, that is, occurrence of two out of the three components of the triad.…”

“…These may have a negative impact on future fertility. Recurrent cyclic abdominal pain, dysmenorrhoea, enlarging lower abdominal mass, 3 coital difficulty, and abnormal vaginal discharge are various presenting symptoms. The pocketed vaginal collection with degenerated blood products can get secondarily infected giving rise to symptoms of pelvic inflammatory disease.…”

Herlyn- werner- wunderlich syndrome: A rare urogenital anomaly masquerading as acute abdomen

“…The initial presenting signs and symptoms were followed by an incorrect diagnosis by the referring physicians 100% of the time, as also missed by us. 2 The most common clinical presentation is that of pelvic pain shortly after menarche, in association with vaginal or pelvic mass, with normal menstrual periods, as also reported by Jindal et al 3 Rarely, it may present as abnormal discharge, infertility and acute abdomen as well.…”