Uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis: the University of Minnesota experience

Stassart, J.P.; Nagel, Theodore C.; Prem, Konald A.; Phipps, William R.

doi:10.1016/s0015-0282(16)54955-3

Cited by 103 publications

(89 citation statements)

References 9 publications

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“…They are inductor elements for adequate Mullerian ducts fusion. For this reason, embryologic anomaly of one Wolffian ducts may cause unilateral renal agenesis associated with imperforate hemivagina (4,11). This hypothesis is supported by Gruenwald's experiment in chick embryos, where ipsilateral renal and Mullerian duct anomalies were produced following the destruction of the caudal portion of the mesonephros (12).…”

Section: Discussionmentioning

confidence: 84%

Herlyn-Werner-Wunderlich syndrome (uterus didelphys, blind hemivagina and ipsilateral renal agenesis) - a case report

Arıkan¹,

Harma²,

Harma³

et al. 2010

J Turkish German Gynecol Assoc

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Uterovaginal duplication with obstructed hemivagina and ipsilateral renal agenesis is referred to as the Herlyn-Werner-Wunderlich (HWW) syndrome. A 17 year old woman presented with right pelvic pain and dysmenorrhea, present since menarche at 13 and worsening over the past year. Ultrasound examination revealed a right pelvic mass (5x5 cm), double endometrial echoes, and hematocolpos. A right pelvic mass, agenesis of the right kidney, double uterus, and blind hemivagina with hematocolpos were detected by magnetic resonance imaging and intravenous pyelography. A right tubo-ovarian abscess with dense adhesions and a double uterus were observed on diagnostic laparoscopy. Adhesiolysis was carried out and purulent material irrigated. After a course of antibiotics, a vaginal septum resection was performed and the pyocolpos drained. She remained symptom free after four months of follow-up. Prompt and accurate diagnosis and treatment of this syndrome can significantly improve the lives of sufferers and prevent future complications. (J Turkish-German Gynecol Assoc 2010; 11: 107-9)

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Section: Discussionmentioning

confidence: 84%

Herlyn-Werner-Wunderlich syndrome (uterus didelphys, blind hemivagina and ipsilateral renal agenesis) - a case report

Arıkan¹,

Harma²,

Harma³

et al. 2010

J Turkish German Gynecol Assoc

View full text Add to dashboard Cite

show abstract

“…Surgical reconstruction of the internal genitalia with restoration of menses and maintenance of a patent genital tract is challenging. Full excision and marsupialisation of the vaginal septum are the preferred surgical approaches for the treatment of uterine didelphys with obstructed unilateral vagina (13). This can be challenging as haematocolpos causes distortion of the adjacent anatomic structures and there is chronic inflammation.…”

Section: Discussionmentioning

confidence: 99%

Uterus didelphys with an obstructed unilateral vagina and ipsilateral renal agenesis: A rare cause of dysmenorrhoea

Attar¹,

Yıldırım²,

Inan³

et al. 2013

J Turkish German Gynecol Assoc

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“…Didelphic uterus with blind hemivagina is a rare congenital malformation that usually coexists with malformations of the urinary tract such as renal agenesis, hypoplasia, dysplasia, or ectopic ureter [2,3]. Uterus didelphys represents 11.1% of uterine anomalies and in most cases a vaginal septum is present.…”

Section: Discussionmentioning

confidence: 99%

“…Typically, patients with an obstructing Müllerian anomaly present after menarche, with dysmenorrhea, severe pelvic or abdominal pain, or the presence of a pelvic or intraabdominal mass [3,11,12]. Other signs and symptoms vary depending on the individual patient's uterovaginal anatomy and may include fever, signs of intra-abdominal infection or purulent vaginal discharge (due to pyocolpos), urinary incontinence, and dyspareunia [1,13,14].…”

Section: Discussionmentioning

confidence: 99%

“…Resection of the obstructive vaginal septum with marsupialization of the margins is the established treatment of didelphic uterus with blind hemivagina since drainage alone may lead to spontaneous closure and subsequent reformation of hemato-or pyocolpos [3,8,11]. This procedure allows evacuation of the sequestered material and preserves reproductive potential [8].…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

A case of didelphic uterus and blind hemivagina with renal dysplasia and ectopic ureter presenting with vulvodynia and recurrent fever

et al. 2009

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Didelphic uterus with blind hemivagina and ipsilateral renal anomaly is a rare congenital malformation. The pathogenesis of this syndrome and its embryologic origin are still the subject of discussion. Due to the variable clinical picture and low index of suspicion, diagnosis is often delayed or inaccurate. Conservative surgical treatmentexcision of the obstructing vaginal septum and marsupialization of the blind hemivagina-is considered the most appropriate treatment. This report describes the case of a 16-year-old girl with didelphic uterus and double vagina, with obstruction of the left hemivagina. The patient was also diagnosed with left renal dysplasia and ipsilateral ureter communication with the obstructed vagina. Following various examinations and left uretero-nephrectomy, the patient was effectively treated with resection of the vaginal septum.

show abstract

Uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis: the University of Minnesota experience

Cited by 103 publications

References 9 publications

Herlyn-Werner-Wunderlich syndrome (uterus didelphys, blind hemivagina and ipsilateral renal agenesis) - a case report

Herlyn-Werner-Wunderlich syndrome (uterus didelphys, blind hemivagina and ipsilateral renal agenesis) - a case report

Uterus didelphys with an obstructed unilateral vagina and ipsilateral renal agenesis: A rare cause of dysmenorrhoea

A case of didelphic uterus and blind hemivagina with renal dysplasia and ectopic ureter presenting with vulvodynia and recurrent fever

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