Urticaria Pigmentosa and Polycythaemia Vera

Polycythaemia Vera and Lymphogranuloma

“…The latter may be caused: 1) by the evolution of the polycythaemia into a myelofibrosis, which is well-known (22)(23)(24)(25) and considered a late stage of the po lycythaemia (11); 2) by the ray-treatment applied. In our case the irradiation of the cervical areae does not come into question, be cause the anaemia existed prior to it.…”

Urticaria pigmentosa with concomitant polycythaemia vera in a 3-year-old boy

“…2 Polycythaemia vera (PV), a myeloproliferative neoplasm, has been reported in only a few adult UP cases. 3 We report a case of childhood UP occurring concomitantly with PV.…”

“…Haematological neoplasms, such as chronic myelomonocytic leukaemia, myelodysplastic syndrome and myeloproliferative neoplasms, occur rarely in patients with mastocytosis . Polycythaemia vera (PV), a myeloproliferative neoplasm, has been reported in only a few adult UP cases . We report a case of childhood UP occurring concomitantly with PV.…”

“…Haematological disorders have been reported rarely in association with UP. 3 PV is an extremely rare disease in children, with only 1% of patients presenting before the age of 25 years, and only 0.1% being younger than 20 years. 4 Hence, there is little available literature discussing paediatric PV, and to our knowledge, ours is the first reported case of concomitant childhood UP.…”

“…Haematological disorders have been reported rarely in association with UP . PV is an extremely rare disease in children, with only 1% of patients presenting before the age of 25 years, and only 0.1% being younger than 20 years .…”