Unusual presentation of a retinoblastoma: A rare case

Abstract

Introduction: Although a retinoblastoma is a well recognized condition it is still associated with a high mortality rate especially in developing countries because partly patients tend to present at very late stages to the health facilities. the mean age of occurrence of a retinoblastoma is 18 months and the age range of a retinoblastoma occurrence is 0-5 years. Diagnosing a retinoblastoma above the age of six years is extremely rare and exceptional. case report: An eight-year-old girl was presented with a six-month history of a fast growing right eye mass and proptosis. the mass was fungating and septic. the patient had normal developmental milestones. At presentation the body weight 21.40 kg.the vital signs were within normal limits (temperature 36.8°c, pulse 83 beats/min, blood pressure 116/77 mmHg). the diagnosis of a retinoblastoma was highly suspected on clinical and radiological imaging but due to patient's age there was also a suspicion of a rhabdomyosarcoma of the orbit. biopsy was performed and the diagnosis of a retinoblastoma was confirmed and the patient was then started on chemotherapy. the patient later demised