Unusual Presentation Chronic Pulmonary Embolism due to Calcified Right Ventricular Mass

Hyun, Yu Kyung; Cho, Yun Hyeong; Lee, Buhyun; Park, Hyung Bok

doi:10.4250/jcu.2011.19.2.91

Cited by 4 publications

(1 citation statement)

References 10 publications

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“…Restrictive cardiomyopathy treatment aims to reduce heart failure symptoms. Routine therapy includes diuretic therapy, ACE inhibitors or angiotensin II receptor antagonists, beta-blockers, digitalis, and anticoagulants to prevent thrombosis [ 12 – 14 ]. There are different approaches to the indications for surgical treatment and the timing of its implementation.…”

Section: Discussionmentioning

confidence: 99%

Successful One-and-a-Half Ventricle Repair of Right Ventricle Dysfunction Due to Lymphoblastic Leukemia Treatment in a Patient with Restrictive Cardiomyopathy

et al. 2021

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Patient: Female, 29-year-old Final Diagnosis: Restrictive cardiomyopathy with isolated endomyocardial fibrosis of the right ventricle • tricuspid valve insufficiency Symptoms: Reduced exercise tolerance • dyspnea and heart rhythm disorders Medication: — Clinical Procedure: — Specialty: Cardiac Surgery • Cardiology Objective: Rare disease Background: The cardiotoxic effects of chemotherapy in cancer treatment can damage cardiomyocytes. A common link in the pathogenesis is the proliferation of fibroblasts and the increase of collagen synthesis, leading to development of common endomyocardial fibrosis. The walls of ventricles become rigid and their inability to relax prevents them from carrying the required amount of blood. The myocardial contractility gradually decreases and leads to ventricular dysfunction and signs of heart failure. Case Report: A 29-year-old woman with reduced exercise tolerance, dyspnea, and heart rhythm disorders was admitted to our hospital. Lymphoblastic leukemia had been diagnosed at the age of 8 years, and she underwent 8 courses of polychemotherapy. She had normal heart anatomy. At the current admission, the diagnostic protocol included echocardiography, computed tomography, cardiac catheterization, and angiocardiography. She was diagnosed with restrictive cardiomyopathy with isolated endomyocardial fibrosis of the right ventricle, and moderate tricuspid valve insufficiency NYHA class III. The patient underwent a right-sided bidirectional cavopulmonary connection with tricuspid valve repair. The early postoperative period was uneventful, and SVCp decreased to 14 mmHg. At discharge, the patient’s clinical condition had improved and tricuspid regurgitation was minimal. Conclusions: The one-and-a-half ventricular correction, commonly used in patients with Ebstein’s anomaly and RV dysfunction or in patients with congenital heart defects associated with RV hypoplasia, is proposed as the method of choice for cardiomyopathy type RV dysfunction.

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Section: Discussionmentioning

confidence: 99%

Successful One-and-a-Half Ventricle Repair of Right Ventricle Dysfunction Due to Lymphoblastic Leukemia Treatment in a Patient with Restrictive Cardiomyopathy

et al. 2021

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Surgical excision of a giant calcified amorphous tumour of the right ventricle and right pulmonary artery

Prifti

Kajo

Krakulli

et al. 2015

Interact CardioVasc Thorac Surg

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A cardiac calcified amorphous tumour (CCAT) is a rare non-neoplastic intracavitary mass with unknown causes. We describe a 32-year old male presenting with progressive dyspnoea, cough and oedemas. The transthoracic echocardiography and contrast-enhanced angio-computed tomography demonstrated a 4 × 10 cm calcified mass into the right ventricle and total occlusion of the right pulmonary artery. The patient underwent successful total removal of the mass through a transverse right ventriculotomy, and right pulmonary embolectomy. Histopathological examination of mass confirmed the diagnosis of a CCAT. The postoperative course was uneventful. To our knowledge, this is the first reported case with a confirmed diagnosis of CCAT at two different locations and the third undergoing a combined approach aiming at total mass excision.

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Clinical Features of Cardiac Calcified Amorphous Tumor: A Narrative Review

Takahashi,

Inaba,

Tsuchiya

et al. 2024

Cardiology in Review

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A cardiac calcified amorphous tumor (CAT) is a non-neoplastic cardiac mass composed of calcified nodules surrounded by amorphous fibrous tissue in a context of degeneration and chronic inflammation. Although CAT cases are increasingly reported, its clinical manifestation remains unclear. We aimed to conduct a narrative review of CAT and identify its clinical characteristics. We conducted a comprehensive literature search using PubMed, with the keyword “Cardiac Calcified Amorphous Tumor” to identify relevant articles. A total of 113 articles published between 1997 and 2022 were retrieved. The clinical features allowing for assess patient background, differences with and without end-stage renal disease (ESRD), symptom-related factors, risk factors for embolism caused by CAT, and features of CAT, such as shape, location, mobility, pathology, and treatment, were statistically analyzed in 106 criteria-matched cases. The mean patient age was 60.2 ± 18.6 years, with 45 men and 61 women. Of the data collected from 21 countries, 52 patients were from Japan. Mobile CAT was more common in the chronic renal failure group. Linear, club-shaped, and spindle-shaped CAT tended to be mobile and more common in the ESRD group as well as located in the mitral valve region. The shape, mobility, location, and underlying mechanism of CAT depended on the presence or absence of ESRD. The risk of embolism was considered high because mobile CAT was more common in the ESRD group, and CAT originated in the mitral valve region. Hence, early diagnosis based on periodic examination in patients with ESRD and aggressive surgical treatment are necessary.

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Unusual Presentation Chronic Pulmonary Embolism due to Calcified Right Ventricular Mass

Cited by 4 publications

References 10 publications

Successful One-and-a-Half Ventricle Repair of Right Ventricle Dysfunction Due to Lymphoblastic Leukemia Treatment in a Patient with Restrictive Cardiomyopathy

Successful One-and-a-Half Ventricle Repair of Right Ventricle Dysfunction Due to Lymphoblastic Leukemia Treatment in a Patient with Restrictive Cardiomyopathy

Surgical excision of a giant calcified amorphous tumour of the right ventricle and right pulmonary artery

Clinical Features of Cardiac Calcified Amorphous Tumor: A Narrative Review

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