Bicuspid aortic valve (BAV) is the most common form of congenital heart disease and frequently leads to premature valvular dysfunction. BAV is associated with aortic wall abnormalities and a high prevalence of ascending aorta dilatation and coarctation of the aorta (CoA). Consequently, in patients with BAV a careful assessment of the valve, and also of the aortic root and the ascending aorta, should be performed. The most feared complication is aortic dissection, however, the actual incidence of this complication is low. We report the case of a 58-year-old man who presented with New York Heart Association class III heart failure. The work-up revealed BAV with severe stenosis and severe compromise of left ventricle systolic function. In addition, CoA in the isthmus region, and type B dissection of the aorta were diagnosed.
K E Y W O R D Saortic dissection, bicuspid aortic valve, coarctation of the aorta, heart failure Bicuspid aortic valve (BAV) is the most common form of congenital heart disease (0.5-2%) 1 and is associated with aortic wall abnormalities, including ascending aortic dilatation and coarctation of the aorta (CoA), probably due to a common underlying developmental defect involving the aortic valve and the aortic wall. Consequently, in patients with BAV a careful assessment of the valve, and also of the aortic root and the ascending aorta, should be performed. 2 The most feared complication is aortic dissection, however, the actual incidence of this complication is low (4%). 3,4 We report the case of a 58-year-old man with a history of a "cardiac murmur" since adolescence.