Univentricular Heart

Kreutzer, Jacqueline; Viegas, César; Kreutzer, Eduardo A.; Kreutzer, Guillermo

doi:10.1002/9781444398786.ch39

Cited by 1 publication

(1 citation statement)

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“…Typical examples are tricuspid atresia, mitral atresia, hearts with two atrio-ventricular valves opening into one ventricle (e.g., double inlet left ventricle, double inlet right ventricle), hearts with hypoplastic ventricles (e.g., pulmonary atresia with intact ventricular septum, hypoplastic left heart syndrome), or other rare cardiac defects (e.g., heterotaxy syndromes). Associated are often abnormalities of the great arteries and veins (e.g., transposition of great arteries, systemic or pulmonary vein anomalies, coarctation of the aorta) as well as abnormalities of the atrioventricular (AV) valves (1,2).…”

Section: Introductionmentioning

confidence: 99%

Clinical aspects and targeted inspiratory muscle training in children and adolescents with Fontan circulation: a randomized controlled trial

Neidenbach¹,

Freilinger²,

Stocker³

et al. 2023

Cardiovasc Diagn Ther

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Background: Since 1968, thousands of patients with a morphologically or functionally univentricular heart have been treated with a total cavopulmonary connection/Fontan operation. Because of the resulting passive pulmonary perfusion, blood flow is assisted by the pressure shift during respiration. Respiratory training is known to improve exercise capacity and cardiopulmonary function. However, there are limited data on whether respiratory training can also improve physical performance after Fontan surgery. The aim of the present study was to clarify the effects of six months of daily home-based inspiratory muscle training (IMT) aimed at increasing physical performance by strengthening respiratory muscles, improving lung function and peripheral oxygenation. Methods: In this non-blinded randomized controlled trial, the effects of IMT on lung capacity and exercise capacity were measured in a large cohort of 40 Fontan patients (25% female; 12.3±2.2 years) who were under regular follow-up by the outpatient clinic of the Department of Congenital Heart Defects and Pediatric Cardiology of the German Heart Center Munich. After a lung function test and a cardiopulmonary exercise test, patients were randomly assigned in a parallel arm design to either an intervention group (IG) or a control group (CG) via stratified and computer-generated letter randomization from May 2014 to May 2015. The IG completed a daily, telephone-monitored IMT of three sets of 30 repetitions for six months with an inspiratory resistive training device (POWERbreathe medic ® ), the CG continued their usual daily activities without an IMT until the second examination within the timeframe of

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Section: Introductionmentioning

confidence: 99%